Modern approaches to surgical treatment of children with osteogenesis imperfecta
- Authors: Solodovnikova E.N.1, Zherdev K.V.1, Chelpachenko O.B.1, Ovechkina A.A.1, Yatsyk S.P.1, Timofeev I.V.1
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Affiliations:
- National Medical Research Center of Children's Health
- Issue: No 3 (2021)
- Pages: 265-270
- Section: Articles
- URL: https://pediatria.orscience.ru/2658-6630/article/view/100482
- DOI: https://doi.org/10.26442/26586630.2021.3.200896
- ID: 100482
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Abstract
Osteogenesis imperfecta (OI) is a heterogeneous group of diseases with different types of inheritance, characterized by frequent fractures and deformities of the bone skeleton. Conservative and surgical treatment of children with this pathology is an integral part of a multidisciplinary approach. In the surgical treatment of bone deformities in children with OI, the method of choice is corrective osteotomies, and an effective method of fixation is intramedullary osteosynthesis. Surgical treatment of children with OI is aimed at reducing the number of fractures, correcting deformities and increasing motor activity. Aim of the study to determine the indications for intramedullary osteosynthesis of long tubular bones in children with the disease. To review the studies concerning treatment of children with OI. Consider the different types of metal fixers, their advantages and disadvantages. Today the technique of intramedullary fixation is the "gold" standard in the surgical treatment of children with OI. There is a clear advantage of telescopic rods in terms of the frequency of reoperations, but their use does not exclude the presence of postoperative complications.
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About the authors
Ekaterina N. Solodovnikova
National Medical Research Center of Children's Health
Email: katakrylova0701@gmail.com
ORCID iD: 0000-0002-8519-1445
Graduate Student, National Medical Research Center of Children's Health
Russian Federation, MoscowKonstantin V. Zherdev
National Medical Research Center of Children's Health
Email: drzherdev@mail.ru
ORCID iD: 0000-0003-3698-6011
D. Sci. (Med.), National Medical Research Center of Children's Health
Russian Federation, MoscowOleg B. Chelpachenko
National Medical Research Center of Children's Health
Author for correspondence.
Email: Chelpachenko81@mail.ru
ORCID iD: 0000-0002-0333-3105
D. Sci. (Med.), National Medical Research Center of Children's Health
Russian Federation, MoscowAnna A. Ovechkina
National Medical Research Center of Children's Health
Email: asha83@yandex.ru
Graduate Student, National Medical Research Center of Children's Health
Russian Federation, MoscowSergey P. Yatsyk
National Medical Research Center of Children's Health
Email: makadamia@yandex.ru
ORCID iD: 0000-0001-6966-1040
D. Sci. (Med.), Prof., Corr. Memb. RAS. National Medical Research Center of Children's Health
Russian Federation, MoscowIgor V. Timofeev
National Medical Research Center of Children's Health
Email: doktor_timofeev@mail.ru
ORCID iD: 0000-0002-4662-2089
Cand. Sci. (Med.), National Medical Research Center of Children's Health
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